D56.0

ICD-10Billable

Alpha thalassemia

Official ICD-10-CM descriptor (FY2026)

Alpha thalassemia

D56.0 is valid for submission on a claim — CMS flags it as a billable, specific code.

Inclusion terms

  • Alpha thalassemia major
  • Hemoglobin H Constant Spring
  • Hemoglobin H disease
  • Hydrops fetalis due to alpha thalassemia
  • Severe alpha thalassemia
  • Triple gene defect alpha thalassemia

Excludes1

Not coded here. An Excludes1 code should never be reported at the same time as the code above it.

  • alpha thalassemia trait or minor (D56.3)
  • asymptomatic alpha thalassemia (D56.3)
  • hydrops fetalis due to isoimmunization (P56.0)
  • hydrops fetalis not due to immune hemolysis (P83.2)

Use additional code

Report an additional code to identify the associated condition.

  • code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)

Related codes in D56

Where this code sits

Parent code
D56

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Source

ICD-10-CM FY2026. Centers for Medicare & Medicaid Services (CMS) / National Center for Health Statistics (NCHS), “2026 ICD-10-CM Code Descriptions in Tabular Order” (icd10cm_order_2026.txt). Download the original file from cms.gov. Public domain (US Government work). Descriptors, billable flags and instructional notes on this page are reproduced from that file without modification. Krasyn adds no clinical guidance.

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