D59.5
ICD-10BillableParoxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
Official ICD-10-CM descriptor (FY2026)
Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
D59.5 is valid for submission on a claim — CMS flags it as a billable, specific code.
Excludes1
Not coded here. An Excludes1 code should never be reported at the same time as the code above it.
- hemoglobinuria NOS (R82.3)
Related codes in D59
- D59.0Drug-induced autoimmune hemolytic anemia
- D59.1Other autoimmune hemolytic anemiascategory
- D59.2Drug-induced nonautoimmune hemolytic anemia
- D59.3Hemolytic-uremic syndromecategory
- D59.4Other nonautoimmune hemolytic anemias
- D59.6Hemoglobinuria due to hemolysis from other external causes
- D59.8Other acquired hemolytic anemias
- D59.9Acquired hemolytic anemia, unspecified
Where this code sits
- Parent code
- D59
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ICD-10-CM FY2026. Centers for Medicare & Medicaid Services (CMS) / National Center for Health Statistics (NCHS), “2026 ICD-10-CM Code Descriptions in Tabular Order” (icd10cm_order_2026.txt). Download the original file from cms.gov. Public domain (US Government work). Descriptors, billable flags and instructional notes on this page are reproduced from that file without modification. Krasyn adds no clinical guidance.