D76.1

ICD-10Billable

Hemophagocytic lymphohistiocytosis

Official ICD-10-CM descriptor (FY2026)

Hemophagocytic lymphohistiocytosis

D76.1 is valid for submission on a claim — CMS flags it as a billable, specific code.

Inclusion terms

Familial hemophagocytic reticulosis
Histiocytoses of mononuclear phagocytes

Related codes in D76

Where this code sits

Chapter: 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block: Other disorders of blood and blood-forming organs (D70-D77)
Parent code: D76

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Source

ICD-10-CM FY2026. Centers for Medicare & Medicaid Services (CMS) / National Center for Health Statistics (NCHS), “2026 ICD-10-CM Code Descriptions in Tabular Order” (icd10cm_order_2026.txt). Download the original file from cms.gov. Public domain (US Government work). Descriptors, billable flags and instructional notes on this page are reproduced from that file without modification. Krasyn adds no clinical guidance.