E74.4
ICD-10BillableDisorders of pyruvate metabolism and gluconeogenesis
Official ICD-10-CM descriptor (FY2026)
Disorders of pyruvate metabolism and gluconeogenesis
E74.4 is valid for submission on a claim — CMS flags it as a billable, specific code.
Inclusion terms
- Deficiency of phosphoenolpyruvate carboxykinase
- Deficiency of pyruvate carboxylase
- Deficiency of pyruvate dehydrogenase
Excludes1
Not coded here. An Excludes1 code should never be reported at the same time as the code above it.
- disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
- Leigh's syndrome (G31.82)
Related codes in E74
- E74.0Glycogen storage diseasecategory
- E74.1Disorders of fructose metabolismcategory
- E74.2Disorders of galactose metabolismcategory
- E74.3Other disorders of intestinal carbohydrate absorptioncategory
- E74.8Other specified disorders of carbohydrate metabolismcategory
- E74.9Disorder of carbohydrate metabolism, unspecified
Where this code sits
- Parent code
- E74
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ICD-10-CM FY2026. Centers for Medicare & Medicaid Services (CMS) / National Center for Health Statistics (NCHS), “2026 ICD-10-CM Code Descriptions in Tabular Order” (icd10cm_order_2026.txt). Download the original file from cms.gov. Public domain (US Government work). Descriptors, billable flags and instructional notes on this page are reproduced from that file without modification. Krasyn adds no clinical guidance.