E77.0
ICD-10BillableDefects in post-translational mod of lysosomal enzymes
Official ICD-10-CM descriptor (FY2026)
Defects in post-translational modification of lysosomal enzymes
E77.0 is valid for submission on a claim — CMS flags it as a billable, specific code.
Inclusion terms
- Mucolipidosis II [I-cell disease]
- Mucolipidosis III [pseudo-Hurler polydystrophy]
Related codes in E77
Where this code sits
- Parent code
- E77
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ICD-10-CM FY2026. Centers for Medicare & Medicaid Services (CMS) / National Center for Health Statistics (NCHS), “2026 ICD-10-CM Code Descriptions in Tabular Order” (icd10cm_order_2026.txt). Download the original file from cms.gov. Public domain (US Government work). Descriptors, billable flags and instructional notes on this page are reproduced from that file without modification. Krasyn adds no clinical guidance.