E78.1
ICD-10BillablePure hyperglyceridemia
Official ICD-10-CM descriptor (FY2026)
Pure hyperglyceridemia
E78.1 is valid for submission on a claim — CMS flags it as a billable, specific code.
Inclusion terms
- Elevated fasting triglycerides
- Endogenous hyperglyceridemia
- Fredrickson's hyperlipoproteinemia, type IV
- Hyperlipidemia, group B
- Hyperprebetalipoproteinemia
- Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia
Related codes in E78
- E78.0Pure hypercholesterolemiacategory
- E78.2Mixed hyperlipidemia
- E78.3Hyperchylomicronemia
- E78.4Other hyperlipidemiacategory
- E78.5Hyperlipidemia, unspecified
- E78.6Lipoprotein deficiency
- E78.7Disorders of bile acid and cholesterol metabolismcategory
- E78.8Other disorders of lipoprotein metabolismcategory
- E78.9Disorder of lipoprotein metabolism, unspecified
Where this code sits
- Parent code
- E78
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ICD-10-CM FY2026. Centers for Medicare & Medicaid Services (CMS) / National Center for Health Statistics (NCHS), “2026 ICD-10-CM Code Descriptions in Tabular Order” (icd10cm_order_2026.txt). Download the original file from cms.gov. Public domain (US Government work). Descriptors, billable flags and instructional notes on this page are reproduced from that file without modification. Krasyn adds no clinical guidance.