G11.3
ICD-10BillableCerebellar ataxia with defective DNA repair
Official ICD-10-CM descriptor (FY2026)
Cerebellar ataxia with defective DNA repair
G11.3 is valid for submission on a claim — CMS flags it as a billable, specific code.
Inclusion terms
- Ataxia telangiectasia [Louis-Bar]
Excludes2
Not included here. The condition is not part of this code, but a patient may have both, and both codes may be reported together.
- Cockayne's syndrome (Q87.19)
- other disorders of purine and pyrimidine metabolism (E79.-)
- xeroderma pigmentosum (Q82.1)
Related codes in G11
- G11.0Congenital nonprogressive ataxia
- G11.1Early-onset cerebellar ataxiacategory
- G11.2Late-onset cerebellar ataxia
- G11.4Hereditary spastic paraplegia
- G11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontia
- G11.6Leukodystrophy with vanishing white matter disease
- G11.8Other hereditary ataxias
- G11.9Hereditary ataxia, unspecified
Where this code sits
- Parent code
- G11
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ICD-10-CM FY2026. Centers for Medicare & Medicaid Services (CMS) / National Center for Health Statistics (NCHS), “2026 ICD-10-CM Code Descriptions in Tabular Order” (icd10cm_order_2026.txt). Download the original file from cms.gov. Public domain (US Government work). Descriptors, billable flags and instructional notes on this page are reproduced from that file without modification. Krasyn adds no clinical guidance.