I27.0
ICD-10BillablePrimary pulmonary hypertension
Official ICD-10-CM descriptor (FY2026)
Primary pulmonary hypertension
I27.0 is valid for submission on a claim — CMS flags it as a billable, specific code.
Inclusion terms
- Heritable pulmonary arterial hypertension
- Idiopathic pulmonary arterial hypertension
- Primary group 1 pulmonary hypertension
- Primary pulmonary arterial hypertension
Excludes1
Not coded here. An Excludes1 code should never be reported at the same time as the code above it.
- persistent pulmonary hypertension of newborn (P29.30)
- pulmonary hypertension NOS (I27.20)
- secondary pulmonary arterial hypertension (I27.21)
- secondary pulmonary hypertension (I27.29)
Related codes in I27
Where this code sits
- Parent code
- I27
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ICD-10-CM FY2026. Centers for Medicare & Medicaid Services (CMS) / National Center for Health Statistics (NCHS), “2026 ICD-10-CM Code Descriptions in Tabular Order” (icd10cm_order_2026.txt). Download the original file from cms.gov. Public domain (US Government work). Descriptors, billable flags and instructional notes on this page are reproduced from that file without modification. Krasyn adds no clinical guidance.